Prosthetic rehabilitation of a 3 year old child with Hypohidrotic Ectodermal Dysplasia

Abstract

Hypohidrotic ectodermal dysplasia (DEH) or Christ-Siemens-Touraine Syndrome is a rare congenital disease, in which is affected one or more ectodermic tissue components and is characterized by hypohidrosis, hypotrichosis and hypodontia. Most cases are associated with X-linked recessive heredity, thus affecting in males, but there are other forms of dominant and recessive autosomal heredity. We report the case of a child of 3 years 5 months with oligodontia and resorption of alveolar processes by absence of deciduous teeth, so that makes prosthetic rehabilitation with removable full dentures, as a result is achieved an increasing of the vertical dimension, improved phonation, mastication, speech and self-esteem.