Langerhans Cell Histiocytosis

Authors

  • Renata Da Fonseca
  • Lydia López Del-Valle
  • Lis Arocho
  • Diego González
  • José González
  • Edgar Perales de Anda
  • Damaris Molina-Negrón

DOI:

https://doi.org/10.47990/alop.v7i2.141

Keywords:

infants, Langerhans cell histiocytosis, periodontitis, oral manifestations

Abstract

Langerhans cell histiocytosis (LCH) is a rare idiopathic disease characterized by the clonal proliferation of Langerhans cells. LCH may appear as a single osteolytic lesion or can affect many body systems. Oral involvement may predate systemic manifestations or mimic infectious/inflammatory disorders. This case report involves a 3-year-old boy referred to the pediatric dentistry residency clinic at the University of Puerto Rico to evaluate possible periodontal disease on primary second lower molars. Examination revealed bilateral extra-oral swelling on the left and right side of the face obliterating the mandibular angles. The overlying skin was intact and symptomless. An intraoral examination showed localized swelling of the overlying mucosa from the lower primary right and left molars with some degree of mobility on both the right and left second primary molars. This case illustrates the need for pediatricians and pediatric dentists to be aware of LCH mimicking periodontal lesions.

References

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Published

2021-01-21

Issue

Section

Case report

How to Cite

Langerhans Cell Histiocytosis. (2021). Latin American Pediatric Dentistry Journal, 7(2). https://doi.org/10.47990/alop.v7i2.141