Manejo de secuelas de defectos del esmalte en paciente con Síndrome Muenke: Reporte de caso

Anahí Francisca Huamán Ochoa; Gilmer Torres Ramos; María  Medrano Hernández; Roxana Patricia López Ramos

doi:10.47990/alop.v11i2.247

Autores

Anahí Francisca Huamán Ochoa Universidad Nacional Mayor de San Marcos https://orcid.org/0000-0001-7073-1771
Gilmer Torres Ramos Universidad Nacional Mayor de San Marcos
María Medrano Hernández Universidad Nacional Mayor de San Marcos
Roxana Patricia López Ramos Univerdidad Peruana Cayetano Heredia https://orcid.org/0000-0003-4374-9575

DOI:

https://doi.org/10.47990/alop.v11i2.247

Palavras-chave:

esmalte dentario, hipoplasia do esmalte dentario, síndrome, craniossinostose

Resumo

Resumo:

O síndrome Muenke é caracterizado por atraso no desenvolvimento e perda auditiva neurossensorial. Pessoas com síndrome podem ter defeitos de desenvolvimento do esmalte. No entanto, em pessoas com síndrome Muenke não há evidências sobre o manejo das sequelas desses defeitos. Objetivo: Descrever o manejo das sequelas de defeitos de desenvolvimento do esmalte em dentes decíduos com um procedimento odontológico abrangente na sala de cirurgia de um paciente com síndrome Muenke. Caso Clínico: Paciente masculino de 2 anos com diagnóstico sistêmico de Síndrome Muenke e diagnóstico dentário: Fraturas pós-eruptivas da extensão do defeito de esmalte I (< 1/3 do dente) e II (1 / 3 - 2/3 do dente) nos dentes anteriores inferiores. e fraturas pós-eruptivas da extensão do defeito de esmalte III (> 2/3 do dente) dos dentes 62 e 52. Os tratamentos realizados foram com resina compostas fotopolimerizáveis que permitiu restaurar as fraturas pós-eruptivas da extensão I e II do defeito do esmalte dos dentes anteriores inferiores. Nos dentes 62 e 52 com fraturas pós-eruptivas do defeito de esmalte de extensão III.foram restauradas com coroas de resina compostas fotopolimerizáveis à mão libre. Conclusão: Os tratamentos foi considerado clinicamente positivo em paciente com Síndrome de Muenke; porque após 6 meses os dentes tratados não apresentavam dor espontânea, nem fístulas ou abscessos, nem mobilidade dentária.

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